Simple gastroschisis complicated by multiple perforations, frozen abdomen, and loss of abdominal domain
DOI:
https://doi.org/10.23938/ASSN.1098Keywords:
Gastroschisis, Intestinal Perforation, Fistula, Jejunostomy, Infants, NewbornAbstract
Gastroschisis is a congenital malformation characterized by a visceral hernia and is one of the leading causes of short bowel syndrome in pediatric patients. This condition can result from congenital short bowel, but may also arise due to complications associated with the management of the abdominal wall defect.
We present the case of a full-term newborn with simple gastroschisis who developed multiple gastrointestinal complications during initial management and was subsequently referred to our institution. On admission, the patient exhibited an open, frozen abdomen, enteroatmospheric fistulas, and loss of abdominal domain. Over the course of three months, various combined techniques were used, including primary intestinal sutures, jejunostomies with distal stoma feedback, botulinum toxin injections, and the construction of a polypropylene silo, with adjustments made based on the evolving complications. Ultimately, complete abdominal reconstruction was achieved. The patient's recovery was favorable, and he was discharged at five months of age with oral tolerance and appropriate weight and height gain.
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