Highly aggressive pulmonary epithelioid hemangioendothelioma: A case report

Authors

  • H. Arasanz Esteban Complejo Hospitalario de Navarra
  • B. Hernández Marín
  • S. Pérez Ricarte
  • A. Lacalle Emborujo
  • L. Pérez Ricarte
  • M. Martínez Aguillo

DOI:

https://doi.org/10.23938/ASSN.0035

Keywords:

Epithelioid hemangioendothelioma. Lung.

Abstract

Pulmonary epithelioid hemangioendothelioma is an uncommon neoplastic disease of endothelial origin, with an incidence inferior to one in a million. It usually behaves as a low-grade malignancy; nevertheless, a few cases have been described in which this tumour manifests a highly aggressive behavior, spreading throughout the organism. We report the case of a 77-year-old woman who was diagnosed with metastatic pulmonary epithelioid hemangioendothelioma with severe symptoms, requiring urgent treatment to palliate them.

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Published

2017-08-31

How to Cite

1.
Arasanz Esteban H, Hernández Marín B, Pérez Ricarte S, Lacalle Emborujo A, Pérez Ricarte L, Martínez Aguillo M. Highly aggressive pulmonary epithelioid hemangioendothelioma: A case report. An Sist Sanit Navar [Internet]. 2017 Aug. 31 [cited 2026 Feb. 12];40(2):309-14. Available from: https://recyt.fecyt.es/index.php/ASSN/article/view/55439

Issue

Section

Clinical notes

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