Non-invasive diagnosis of cardiac amyloidosis due to transthyretin. Case report

Authors

  • M. Povar Echeverría Hospital Universitario Miguel Servet
  • P.E. Auquilla Clavijo Hospital Universitario Miguel Servet
  • J.A. Escobedo Palau Hospital Universitario Miguel Servet
  • P. Navarro Beltrán Hospital Universitario Miguel Servet
  • J. Povar Marco Hospital Universitario Miguel Servet

DOI:

https://doi.org/10.23938/ASSN.0295

Keywords:

Amyloidosis. Transthyretin. Cardiomiopathy. Heart failure. 99mTc-DPD scintigraphy.

Abstract

Amyloidosis due to deposits of transthyretin (ATTR) is currently considered the most frequent form of cardiac amyloidosis and its incidence is increasing thanks to the advances in diagnostic imaging techniques. Some non-invasive diagnostic criteria have recently been published on this entity that due to the development of new drugs for the specific treatment of cardiac ATTR, have prognostic and therapeutic implications. That is why cardiac ATTR could cease to be a rare disease and become a frequent one, and become potentially treatable instead of incurable.

We present the case of an 80-year-old male diagnosed with non-hereditary cardiac ATTR by means of gammagraphy with 99mTc diphosfonate scintigraphy (99mTc-DPD) following the new criteria of non-invasive diagnosis.

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References

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Published

2018-08-29

How to Cite

Povar Echeverría, M., Auquilla Clavijo, P., Escobedo Palau, J., Navarro Beltrán, P., & Povar Marco, J. (2018). Non-invasive diagnosis of cardiac amyloidosis due to transthyretin. Case report. Anales Del Sistema Sanitario De Navarra, 41(2), 263–267. https://doi.org/10.23938/ASSN.0295

Issue

Vol. 41 No. 2 (2018)

Section

Clinical notes

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